Heterotaxy: fluctuat nec mergitur

Abstract The International Pediatric and Congenital Cardiac Code (IPCCC) states that visceral heterotaxy is defined as “a congenital malformation in which the internal thoraco-abdominal organs demonstrate abnormal arrangement across left-right axis of body. By convention, cardiology, syndrome does not include patients with complete mirror-imaged along also known “total mirror imagery” or “situs inversus totalis”.” [ www.ipccc.net ] In heterotaxy, it important to describe both cardiac relations junctional connections segments, documentation atrial appendages, ventricular topology, nature unions segments atrioventricular ventriculoarterial junctions, infundibular morphologies, relationships arterial trunks space. Particular attention required for venoatrial connections, since these are so often abnormal. relationship remaining organs, including lungs, spleen, liver, intestines, must be described separately, because, although common patterns association have been identified, there frequent exceptions patterns. Therefore, each thoracic abdominal organ independently.